The UMD-THAP1 mutations database
Record ID: 48

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.247T>Cp.Cys83ArgHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
TGTCysCGTArgT->CTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
 Yes, coding strandNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.860.35 (non pathogenous)82 (Pathogenous)

Patient and sample data


Sample IDPatient IDFamily IDPatient statusGenderTransmissionGeographic origin
GER02TUE F0007 I0001case 7-ProbandFemaleNo family historyGERMANY

Phenotypic groupDisease
NAFocal dystonia

Clinical data


SymptomSeverityAge
Age at last examination
Age of onsetneck34
Neck34

Reference


Reference IDPubMed IDReference
1220669277
S*hn AS, Gl*ckle N, Doetzer AD, Deuschl G, Felbor U, Topka HR, Sch*ls L, Riess O, Bauer P, MŸller U, Grundmann K. Prevalence of THAP1 sequence variants in German patients with primary dystonia. Mov Disord. 2010 Sep 15;25(12):1982-6.