The UMD-THAP1 mutations database
Record ID: 42

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.169C>Ap.His57AsnHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
CACHisAACAsnC->ATv

StructureKey Residue (HCD)Pyrimidin doubletCpG
H2-THAP dom. C2CH motifNoNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.790.05 (non pathogenous)59 (Probable polymorphism)

Patient and sample data


Sample IDPatient IDFamily IDPatient statusGenderTransmissionGeographic origin
GER02TUE F0001 I0001Case 1-ProbandFemaleNo family historyGERMANY

Phenotypic groupDisease
NAGeneralized dystonia

Clinical data


SymptomSeverity
Age at last examination
Age of onsetleg
Dysarthriamild
Incomplete clinical description
Speechmild

Reference


Reference IDPubMed IDReference
1220669277
S*hn AS, Gl*ckle N, Doetzer AD, Deuschl G, Felbor U, Topka HR, Sch*ls L, Riess O, Bauer P, MŸller U, Grundmann K. Prevalence of THAP1 sequence variants in German patients with primary dystonia. Mov Disord. 2010 Sep 15;25(12):1982-6.