The UMD-THAP1 mutations database
Record ID: 213

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.530T>Cp.Leu177ProHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
CTTLeuCCTProT->CTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Coiled-Coil dom. Yes, coding strandNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): Alu I

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.930.01 (pathogenous)70 (Probably pathogenous)

Patient and sample data


Sample IDPatient IDFamily IDPatient statusGenderTransmissionGeographic origin
AUS01BRI F0001 I0001probandProbandMaleFamilialAUSTRALIA

Phenotypic groupDisease
NAAsymptomatic

Clinical data


Symptom
Asymptomatic

Reference


Reference IDPubMed IDReference
3623649788
Newman JR, Lehn AC, Boyle RS, Silburn PA, Mellick GD. Screening for rare sequence variants in the THAP1 gene in a primary dystonia cohort. Mov Disord. 2013 Oct;28(12):1752-3.