The UMD-THAP1 mutations database
Record ID: 174

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.424A>Gp.Thr142AlaHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
ACAThrGCAAlaA->GTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Coiled-Coil dom. NoNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.930.39 (non pathogenous)65 (Probably pathogenous)

Patient and sample data


Sample IDPatient IDFamily IDPatient statusGenderTransmissionGeographic origin
USA01NYO F0016 I0001ProbandUnknownUnknownU.S.A.

Phenotypic groupDisease
NAUnknown

Clinical data


Symptom
No clinical data available

Reference


Reference IDPubMed IDReference
28 21752024
Sengel C, Gavarini S, Sharma N, Ozelius LJ, Bragg DC. Dimerization of the DYT6 dystonia protein, THAP1, requires residues within the coiled-coil domain. J Neurochem. 2011 Sep;118(6):1087-100.