The UMD-THAP1 mutations database
Record ID: 157

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.521A>Gp.Glu174GlyHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
GAAGluGGAGlyA->GTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Coiled-Coil dom. Yes, non coding strandNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
10.29 (non pathogenous)76 (Pathogenous)

Patient and sample data


Sample IDPatient IDFamily IDPatient statusGenderTransmissionGeographic origin
CHI02CHE F0002 I0001ProbandFemaleNo family historyCHINA

Phenotypic groupDisease
NASegmental dystonia

Clinical data


SymptomSeverityAge
Age at last examination22
Age of onsetneck19
Neck19
Trunk22

Reference


Reference IDPubMed IDReference
21 21839475
Song W, Chen Y, Huang R, Chen K, Pan P, Yang Y, Shang HF. Novel THAP1 gene mutations in patients with primary dystonia from Southwest China. J Neurol Sci. 2011 Oct 15;309(1-2):63-7.