The UMD-MSH2 mutations database
Record ID: 986

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.IVS10-43C>T (c.1662-43C>T)

wt codonwt aamutant codonmutant aamutational eventmutation type
AGCSerspl-43Spl.C>T

StructureKey Residue (HCD)Pyrimidin doubletCpG
EXO1 stabilization 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Alternative Branch Point?
tacacat
70.7 _
taTacat
46.9 _ *
-33.6 %

Patient and sample data


Sample IDPatient status
31_H459_H459-1_H459-1ARelative

Clinical data


Symptom

Reference


Reference IDReference
31Unpublished data