The UMD-MSH2 mutations database
Record ID: 85

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.IVS14-38T>G (c.2459-38T>G)

wt codonwt aamutant codonmutant aamutational eventmutation type
GGTGlyspl-38Spl.T>G

StructureKey Residue (HCD)Pyrimidin doubletCpG
ATPase 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Alternative Branch Point?
ttctcat
94.6 _
ttcGcat
75.7 _ *
-20 %

Patient and sample data


Sample IDPatient status
2_02-DDM4321_1968_19684412Relative

Clinical data


Symptom

Reference


Reference IDReference
2Unpublished data