The UMD-MSH2 mutations database
Record ID: 385

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.IVS4+1G>C (c.792+1G>C)

wt codonwt aamutant codonmutant aamutational eventmutation type
CAGGlnspl+1Spl.G>C

StructureKey Residue (HCD)Pyrimidin doubletCpG
EXO1 stabilization 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
CAGgtacat
79 _
CAGctacat
52.2 _ *
-34 %

Patient and sample data


Sample IDPatient status
6_609091_B00067397_S0077Relative

Clinical data


Symptom

Reference


Reference IDReference
6Unpublished data