The UMD-MSH2 mutations database
Record ID: 1824

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.IVS8+1G>T (c.1386+1G>T)

wt codonwt aamutant codonmutant aamutational eventmutation type
CAGGlnspl+1Spl.G>T

StructureKey Residue (HCD)Pyrimidin doubletCpG
EXO1 stabilization 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
CAGgtatgc
89 _
CAGttatgc
62.2 _ *
-30.1 %

Patient and sample data


Sample IDPatient status
7_-652---E050210Relative

Clinical data


Symptom

Reference


Reference IDReference
7Unpublished data