The UMD-MSH2 mutations database
Record ID: 124

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.IVS4-23G>A (c.793-23G>A)

wt codonwt aamutant codonmutant aamutational eventmutation type
GTTValspl-23Spl.G>A

StructureKey Residue (HCD)Pyrimidin doubletCpG
EXO1 stabilization 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)

Patient and sample data


Sample IDPatient status
2_02-DDM2676_18508_18508Relative

Clinical data


Symptom

Reference


Reference IDReference
2Unpublished data