The UMD-MLH1 mutations database
Record ID: 882

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation status
c.2005G>Cp.Glu669Gln

wt codonwt aamutant codonmutant aamutational eventmutation type
GAAGluCAAGlnG->CTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
MLH3/PMS1/PMS2 interaction Yes, non coding strandNo

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.930.00 (pathogenous)41 (Polymorphism)

Patient and sample data


Sample IDPatient status
31_H1194_H1194-1_H1194-1ARelative

Clinical data


Symptom

Reference


Reference IDReference
31Unpublished data