The UMD-MEN1 mutations database
Record ID: 938

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS9-1G>T (c.1351-1G>T)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
GTGValspl-1Spl.G->TTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
Pem,NM,CH 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Acceptor
ccactggcccagGT
84.9 _
ccactggcccatGT
56 _ *
-34.1 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
03-OL09-M01R-ProbandFemale76

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
1817185897
Tala, H. P., Carvajal, C. A., Gonz‡lez, A. A., Garrido, J. L., Tobar, J., Solar, A., ? Fardella, C. E. (2006). New splicing mutation of MEN1 gene affecting the translocation of menin to the nucleus. Journal of Endocrinological Investigation, 29(10), 888?93. Retrieved from http://www.ncbi.nlm.nih.gov/pubmed/17185897