The UMD-MEN1 mutations database
Record ID: 89

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS4+1G>A (c.783+1G>A)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
CAGGlnspl+1Spl.G->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm,NM,NMH,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
CAGgtgagg
96.9 _
CAGatgagg
70.1 _ *
-27.7 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
04-IB01-F12O-ProbandFemale31

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
510664520
Morelli, A., Falchetti, A., Martineti, V., Becherini, L., Mark, M., Friedman, E., & Brandi, M. L. (2000). MEN1 gene mutation analysis in Italian patients with multiple endocrine neoplasia type 1. European Journal of Endocrinology / European Federation of Endocrine Societies, 142(2), 131?7. Retrieved from http://www.ncbi.nlm.nih.gov/pubmed/10664520