The UMD-MEN1 mutations database
Record ID: 777

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS7+1G>A (c.1049+1G>A)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
GACAspspl+1Spl.G->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Ju,NF,Pem,NM,RP,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
GGAgtgagg
79.7 _
GGAatgagg
52.9 _ *
-33.7 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
03-AU20-R15L-ProbandMale

Phenotypic groupDisease
ModeratePlease contact curator

Reference


Reference IDPubMed IDReference
69463336
Bassett, J. H., Forbes, S. A., Pannett, A. A., Lloyd, S. E., Christie, P. T., Wooding, C., Thakker, R. V. (1998). Characterization of mutations in patients with multiple endocrine neoplasia type 1. American Journal of Human Genetics, 62(2), 232?44. doi:10.1086/301729