The UMD-MEN1 mutations database
Record ID: 450

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.455T>Gp.Leu152TrpHeterozygousLIKELY CAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
TTGLeuTGGTrpT->GTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
Ju, Sm,NM,HD Yes, coding strandNo

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0 - 71 (Probably pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
03-ME20-J15S-ProbandFemale46

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
229709976
Parathyroid MEN1 Gene Mutations in Relation to Clinical Characteristics of Nonfamilial Primary Hyperparathyroidism Tobias Carling, Pamela Correa, Ola Hessman, Jakob Hedberg, Britt Skogseid, Daniel Lindberg, Jonas Rastad, Gunnar Westin, and G*ran *kerstr*m The Journal of Clinical Endocrinology & Metabolism 1998 83:8, 2960-2963