The UMD-MEN1 mutations database
Record ID: 276

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.249_252delGTCTp.Ile85SerfsX33HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
CTGLeudel4cFs.Stop at 117Fr.

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm, NM 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
03-RO13-S05B-RelativeMale26

Phenotypic groupDisease
Not availablePlease contact curator

Reference


Reference IDPubMed IDReference
1210812010
Roijers, J. F., Apel, T., Neumann, H. P., Arnim, U. V, Lips, C. J., & Hoppener, J. W. (2000). Internally shortened menin protein as a consequence of alternative RNA splicing due to a germline deletion in the multiple endocrine neoplasia type 1 gene. International Journal of Molecular Medicine, 5(6), 611?4. Retrieved from http://www.ncbi.nlm.nih.gov/pubmed/10812010