The UMD-MEN1 mutations database
Record ID: 1907

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS3-6C>T (c.655-6C>T)HeterozygousLIKELY CAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
AGCSerspl-6Spl.C->TTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
 

Other variation(s) reported for this sample: c.1252G>A

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Acceptor
tccccccctaagAG
81.6 _
tccccctctaagAG
80.9 _
-0.8 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
02-GE04-J15S-ProbandMale59

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
79683585
Giraud, S., Zhang, C. X., Serova-Sinilnikova, O., Wautot, V., Salandre, J., Buisson, N., ? Calender, A. (1998). Germ-line mutation analysis in patients with multiple endocrine neoplasia type 1 and related disorders. American Journal of Human Genetics, 63(2), 455?67. doi:10.1086/301953