The UMD-MEN1 mutations database
Record ID: 1842

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS3+1G>A (c.654+1G>A)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
CGGArgspl+1Spl.G->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Ju,Sm,NMH,HD,NM 

Other variation(s) reported for this sample: c.61C>A

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
CGGgtattg
72.1 _
CGGatattg
45.3 _ *
-37.2 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
02-SR09-S21G-ProbandFemale30

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
4522275377
Canaff L, Vanbellinghen J-F, Kaji H, Goltzman D, Hendy GN. Impaired Transforming Growth Factor-? (TGF-?) Transcriptional Activity and Cell Proliferation Control of a Menin In-frame Deletion Mutant Associated with Multiple Endocrine Neoplasia Type 1 (MEN1). The Journal of Biological Chemistry. 2012;287(11):8584-8597. doi:10.1074/jbc.M112.341958.