The UMD-MEN1 mutations database
Record ID: 1646

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.842G>Ap.Gly281GluHeterozygousLIKELY CAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
GGGGlyGAGGluG->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Pem,NM,NMH,FA,HD Yes, non coding strandNo

Other variation(s) reported for this sample: c.IVS3-6C>A (c.655-6C>A)

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): Bsu36 I

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0 - 94 (Pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
02-GE18-G12A-ProbandFemale17

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
1316563611
J*ger, A. C., Friis-Hansen, L., Hansen, T. V. O., Eskildsen, P. C., S¿lling, K., Knigge, U., ? Nielsen, F. C. (2006). Characteristics of the Danish families with multiple endocrine neoplasia type 1. Molecular and Cellular Endocrinology, 249(1-2), 123?32. doi:10.1016/j.mce.2006.02.008