The UMD-MEN1 mutations database
Record ID: 1365

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS4-9G>A (c.784-9G>A)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
AAGLysspl-9Spl.G->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm,NM,NMH,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Cryptic Acceptor?
tctctccttcggctc
62.6 _
tctctccttcAgctc
91.5 _ *
31.6 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
01-EL09-K05V-RelativeMale18

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
2810534569
Germline mutations in the MEN1 gene: creation of a new splice acceptor site and insertion of 7 intron nucleotides into the mRNA. Engelbach M1, Forst T, Hankeln T, Tratzky M, Heerdt S, PfŸtzner A, Kann P, Kunt T, Schneider S, Schmidt ER, Beyer J.