The UMD-MEN1 mutations database
Record ID: 1363

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS5-1G>C (c.825-1G>C)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
AGGArgspl-1Spl.G->CTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm,NM,NMH,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Acceptor
atcctttcctagGT
84.5 _
atcctttcctacGT
55.6 _ *
-34.3 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
01-DI05-D05L-ProbandFemale24

Phenotypic groupDisease
StrongPlease contact curator

Reference


Reference IDPubMed IDReference
69463336
Bassett, J. H., Forbes, S. A., Pannett, A. A., Lloyd, S. E., Christie, P. T., Wooding, C., Thakker, R. V. (1998). Characterization of mutations in patients with multiple endocrine neoplasia type 1. American Journal of Human Genetics, 62(2), 232?44. doi:10.1086/301729