The UMD-MEN1 mutations database
Record ID: 1321

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS4-9G>A (c.784-9G>A)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
AAGLysspl-9Spl.G->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm,NM,NMH,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Cryptic Acceptor?
tctctccttcggctc
62.6 _
tctctccttcAgctc
91.5 _ *
31.6 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
01-BR21-J05A-ProbandMale64

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
2715670192
Ellard, S., Hattersley, A. T., Brewer, C. M. and Vaidya, B. (2005), Detection of an MEN1 gene mutation depends on clinical features and supports current referral criteria for diagnostic molecular genetic testing. Clinical Endocrinology, 62: 169?175. doi: 10.1111/j.1365-2265.2005.02190.x