The UMD-MEN1 mutations database
Record ID: 1294

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.IVS4+1G>T (c.783+1G>T)HeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
CAGGlnspl+1Spl.G->TTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
Sm,NM,NMH,FA,HD 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Impact on splicing
Splice site type Wild type sequence CV Mutant type sequence CV Variation (%)
Donor
CAGgtgagg
96.9 _
CAGttgagg
70.1 _ *
-27.7 %

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
01-PO20-M01R-RelativeMale11

Phenotypic groupDisease
asymptomaticPlease contact curator

Reference


Reference IDPubMed IDReference
311836268
Verg*s, B., Boureille, F., Goudet, P., Murat, A., Beckers, A., Sassolas, G., ? Calender, A. (2002). Pituitary disease in MEN type 1 (MEN1): data from the France-Belgium MEN1 multicenter study. The Journal of Clinical Endocrinology and Metabolism, 87(2), 457?65. doi:10.1210/jcem.87.2.8145