The UMD-MEN1 mutations database
Record ID: 1213

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.1413G>Ap.Trp471XHeterozygousCAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
TGGTrpTGAStopG->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Pem,NM,CH Yes, non coding strandNo

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
03-RO21-L01U-ProbandFemale45

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
3210090472
Mutch, M. G., Dilley, W. G., Sanjurjo, F., DeBenedetti, M. K., Doherty, G. M., Wells, S. A., Goodfellow, P. J. and Lairmore, T. C. (1999), Germline mutations in the multiple endocrine neoplasia type 1 gene: Evidence for frequent splicing defects. Hum. Mutat., 13: 175?185. doi: 10.1002/(SICI)1098-1004(1999)13:3<175::AID-HUMU1>3.0.CO;2-R