The UMD-MEN1 mutations database
Record ID: 1

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.65T>Gp.Leu22ArgHeterozygousLIKELY CAUSAL

wt codonwt aamutant codonmutant aamutational eventmutation type
CTGLeuCGGArgT->GTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
Ju, NM, RP Yes, coding strandNo

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): Cfr10 I, Hpa II, Msp I
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0 - 76 (Pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
04-AU07-F01N-ProbandFemale20

Phenotypic groupDisease
SupportingPlease contact curator

Reference


Reference IDPubMed IDReference
29215689
Agarwal, S. K., Kester, M. B., Debelenko, L. V, Heppner, C., Emmert-Buck, M. R., Skarulis, M. C., ? Marx, S. J. (1997). Germline mutations of the MEN1 gene in familial multiple endocrine neoplasia type 1 and related states. Human Molecular Genetics, 6(7), 1169?75. Retrieved from http://www.ncbi.nlm.nih.gov/pubmed/9215689