The UMD-FBN1 mutations database
Record ID: 691

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.718C>Tp.Arg240CysHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
CGCArgTGCCysC->TTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Hybrid module#01 Yes, coding strandYes

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.670.00 (pathogenous)94 (Pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
AUS02WES F0005 I01ProbandNANAAUSTRALIA

Phenotypic groupDisease
NADominant ectopia lentis

Clinical data


Symptom
O-Ectopia lentis

Reference


Reference IDPubMed IDReference
11615054843
Ades LC, Holman KJ, Brett MS, Edwards MJ, Bennetts B. "Ectopia lentis phenotypes and the FBN1 gene". Am J Med Genet. 2004; 126A (3):284-9.