Variation name (cDNA level) | Variation name (protein level) | Variation status | Variation class |
c.3221G>A | p.Cys1074Tyr | Heterozygous | Mutation |
wt codon | wt aa | mutant codon | mutant aa | mutational event | mutation type |
TGC | Cys | TAC | Tyr | G->A | Ts |
Structure | Key Residue (HCD) | Pyrimidin doublet | CpG |
cb EGF-like #12 | Disulfide bonds 1074-1086 (C1) | No | No |
At the mRNA level | On restriction map |
NA | New restriction site(s): none Lost restriction site(s): none |
Conservation (0-1) | SIFT (0-1) | UMD-predictor (0-100) |
---|---|---|
0.83 | 0.00 (pathogenous) | 100 (Pathogenous) |
Sample ID | Patient status | Gender | Transmission | Age of onset | Age of death | Geographic origin |
UKD05LON F0023 I01 | Proband | NA | NA | U.K. |
Phenotypic group | Disease |
NA | Neonatal MFS |
Symptom | Severity |
C-Congestive heart failure | |
C-Mitral regurgitation | |
O-Cataract | |
O-Ectopia lentis | possible |
O-Glaucoma | |
S-Abnormal ears | |
S-Arachnodactyly (M) | |
S-Joint limitations |
Reference ID | PubMed ID | Reference |
109 | 12575662 | Comeglio P, Evans AL, Brice GW, Anderlid BM, Child AH. "Gene symbol: FBN1. Disease: Marfan syndrome". Hum Genet. 2003 Jan;112(1):104. |