Variation name (cDNA level) | Variation name (protein level) | Variation status | Variation class |
c.976delA | p.Thr326ProfsX4 | Heterozygous | Mutation |
wt codon | wt aa | mutant codon | mutant aa | mutational event | mutation type |
ACC | Thr | del1a | Fs. | Stop at 329 | Fr. |
Structure | Key Residue (HCD) | Pyrimidin doublet | CpG |
cb EGF-like #02 |
At the mRNA level | On restriction map |
No mechanism suspected | New restriction site(s): none Lost restriction site(s): none |
Sample ID | Patient status | Gender | Transmission | Age of onset | Age of death | Geographic origin |
USA04NOR F0012 I3524 | Proband | Female | familial | Unknown | U.S.A |
Phenotypic group | Disease |
NA | Classical MFS |
Symptom |
C-Aortic insufficiency |
C-Asc. aortic dilatation |
O-Myopia |
S-Scoliosis > 20° (M)(1) |
Reference ID | PubMed ID | Reference |
102 | - | Hyland JC (Personal communication 2003). |