Variation name (cDNA level) | Variation name (protein level) | Variation status | Variation class |
c.3959G>A | p.Cys1320Tyr | Heterozygous | Mutation |
wt codon | wt aa | mutant codon | mutant aa | mutational event | mutation type |
TGT | Cys | TAT | Tyr | G->A | Ts |
Structure | Key Residue (HCD) | Pyrimidin doublet | CpG |
cb EGF-like #17 | Disulfide bonds 1307-1320 (C6) | No | No |
At the mRNA level | On restriction map |
NA | New restriction site(s): none Lost restriction site(s): Csp6 I, Rsa I |
Conservation (0-1) | SIFT (0-1) | UMD-predictor (0-100) |
---|---|---|
0.83 | 0.00 (pathogenous) | 100 (Pathogenous) |
Sample ID | Patient status | Gender | Transmission | Age of onset | Age of death | Geographic origin |
USA21MIL F0001 I0002 | Relative | Male | familial | U.S.A. |
Phenotypic group | Disease |
NA | Probable MFS |
Symptom |
S-Abnormal ears |
S-Characteristic facial appearance |
Reference ID | PubMed ID | Reference |
257 | 23930893 | Elshershari H, Harris C. "Paternal fibrillin-1 mutation transmitted to an affected son with neonatal marfan syndrome: the importance of early recognition". Cardiol Young. 2013 Aug 9:1-4. |