The UMD-FBN1 mutations database
Record ID: 2873

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.5776A>Gp.Asn1926AspHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
AATAsnGATAspA->GTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
cb EGF-like #28 Yes, non coding strandNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
10.11 (non pathogenous)35 (Polymorphism)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
POR01POR F0010 I0001ProbandFemalede novoPORTUGAL

Phenotypic groupDisease
NAMFS

Clinical data


SymptomAge
C-Asc. aortic dilatation25
C-Mitral valve prolapse25

Reference


Reference IDPubMed IDReference
22422005308
Lebreiro A, Martins E, Cruz C, Almeida J, Pimenta S, Bernardes M, Carlos Machado J, Jœlia Maciel M, Abreu-Lima C. [Genotypic characterization of a Portuguese population of Marfan syndrome patients]. Rev Port Cardiol. 2011 Jul;30(7-8):649-54.