The UMD-FBN1 mutations database
Record ID: 2628

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.7583G>Ap.Cys2528TyrHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
TGCCysTACTyrG->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
cb EGF-like #40 Disulfide bonds 2528-2541 (C1)NoNo

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
10.00 (pathogenous)100 (Pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
FRA01BOU F0887 I0923ProbandFemalefamilialFRANCE

Phenotypic groupDisease
NAMFS

Clinical data


Symptom

Reference


Reference IDPubMed IDReference
207-
Boileau C. (personnal communication 2013)