The UMD-FBN1 mutations database
Record ID: 2482

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.8525_8529delTTAACp.Leu2842ProfsX7HeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
CTTLeudel5bFs.Stop at 2848Fr.

StructureKey Residue (HCD)Pyrimidin doubletCpG
FibuCTDIII-like motif conserved AA fibu Glob DIII

Mutation impact


At the mRNA levelOn restriction map
Deletion flanked by direct repeatsNew restriction site(s): none
Lost restriction site(s): none

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
FRA01BOU F0739 I0776ProbandMaleNAFRANCE

Phenotypic groupDisease
NAMFS

Clinical data


Symptom

Reference


Reference IDPubMed IDReference
207-
Boileau C. (personnal communication 2013)