The UMD-FBN1 mutations database
Record ID: 193

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.4920_4923delTGAAp.Asn1640LysfsX9HeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
AATAsndel4cFs.Stop at 1648Fr.

StructureKey Residue (HCD)Pyrimidin doubletCpG
cb EGF-like #23 

Mutation impact


At the mRNA levelOn restriction map
Deletion of a repeated sequenceNew restriction site(s): none
Lost restriction site(s): none

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
USA08PIT F0012 I01ProbandNANA?U.S.A

Phenotypic groupDisease
NAClassical MFS

Clinical data


Symptom
no clinical data

Reference


Reference IDPubMed IDReference
4910533071
Yuan B, Thomas JP, von Kodolitsch Y, Pyeritz RE. "Comparison of heteroduplex analysis, direct sequencing, and enzyme mismatch cleavage for detecting mutations in a large gene, FBN1". Hum Mutat 1999;14(5):440-6 .