The UMD-FBN1 mutations database
Record ID: 1903

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.718C>Tp.Arg240CysHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
CGCArgTGCCysC->TTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Hybrid module#01 Yes, coding strandYes

Mutation impact


At the mRNA levelOn restriction map
NANew restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.670.00 (pathogenous)94 (Pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
IND01AMR F0001 I0001ProbandMalefamilialINDIA

Phenotypic groupDisease
NADominant ectopia lentis

Clinical data


SymptomAge
O-Ectopia lentis51

Reference


Reference IDPubMed IDReference
17218079676
Vanita V, Singh JR, Singh D, Varon R, Robinson PN, Sperling K. "A recurrent FBN1 mutation in an autosomal dominant ectopia lentis family of Indian origin". Mol Vis. 2007 Oct 25;13:2035-40.