The UMD-F7 mutations database
Record ID: 993

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.160G>Ap.Val54IleHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
GTCValATCIleG->ATs

StructureKey Residue (HCD)Pyrimidin doubletCpG
 Gamma Carboxylation signalNoYes

Other mutation(s) not assigned to a specific allele: c.IVS7+1G>A (c.805+1G>A)

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0.90.00 (pathogenous)53 (Probable polymorphism)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
GR08_082ProbandFemaleVENEZUELA

Phenotypic groupFVII:c level
severe0_<2

c.-323insCCTATATCCT genotypep.Arg413Gln genotype
unknownunknown

Reference


Reference IDPubMed IDReference
6918976247
Herrmann FH, Wulff K, Auerswald G, Schulman S, Astermark J, Batorova A, Kreuz W, Pollmann H, Ruiz-Saez A, De Bosch N, Salazar-Sanchez L; Greifswald Factor FVII Deficiency Study Group. Factor VII deficiency: clinical manifestation of 717 subjects from Europe and Latin America with mutations in the factor 7 gene. Haemophilia. 2009 Jan;15(1):267-80.