The UMD-CSB mutations database
Record ID: 42

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.3715_3716delAAp.Lys1239GlufsX2HomozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
AAGLysdel2aFs.Stop at 1240Fr.

StructureKey Residue (HCD)Pyrimidin doubletCpG
 

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
Meira_COFSProbandCANADA

Phenotypic groupDisease

Clinical data


Symptom

Reference


Reference IDPubMed IDReference
210739753
Meira LB, Graham JM Jr, Greenberg CR, Busch DB, Doughty AT, Ziffer DW, Coleman DM, Savre-Train I, Friedberg EC. Manitoba aboriginal kindred with original cerebro-oculo- facio-skeletal syndrome has a mutation in the Cockayne syndrome group B (CSB) gene. Am J Hum Genet 2000;66(4):1221-8.