The UMD-CSB mutations database
Record ID: 10

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.2058G>Cp.Trp686CysHeterozygousMutation

wt codonwt aamutant codonmutant aamutational eventmutation type
TGGTrpTGCCysG->CTv

StructureKey Residue (HCD)Pyrimidin doubletCpG
 Yes, non coding strandNo

Mutation impact


At the mRNA levelOn restriction map
r.2170_2286delNew restriction site(s): Bsp1286 I, HgiA I
Lost restriction site(s): none

Pathogenicity (bioinformatics predictions)
Conservation (0-1)SIFT (0-1)UMD predictor (0-100)
0 - 71 (Probably pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of deathGeographic origin
CS683VIProbandU.S.A.

Phenotypic groupDisease

Clinical data


Symptom

Reference


Reference IDReference
0Unpublished data